Incontinentia Pigmenti

Document Type: Case Report(s)

Authors

Department of Dermatology, Isfahan University of Medical Sciences, Isfahan

Abstract

Incontinentia pigmenti (IP) is an uncommon X-linked dominant genodermatosis characterized by four cutaneous stages and frequent association with dental (90%), central nervous system (33%) and ocular (35%) anomalies. The exact pathogenesis of this disorder remains unknown.Herein, we report a newborn girl with inflammatory vesiculobullous and warty skin lesions and a positive family history of IP, with blood leucocytosis (eosinophilia and also lymphocytosis), but no other extracutaneous findings.