Intraventricular tuberculoma (IVT) is extremely rare, CT and MRI patterns have been only sparsely described. Herein, a case of intraventricular tuberculoma in a 40 year-old woman is reported. At admission, the patient displayed malaise and was confused and deteriorated suddenly. Brain CT and MRI findings were very similar to intraventricular meningioma. The patient underwent surgery and tuberculoma was removed by transcortical transventricular approach. IVT should be considered in differential diagnosis of intraventricular lesions in endemic areas and in patients with unexplained malaise.