Document Type : Case Report(s)
Authors
Department of Dermatology, Isfahan University of Medical Sciences, Isfahan
Abstract
Incontinentia pigmenti (IP) is an uncommon X-linked dominant genodermatosis characterized by four cutaneous stages and frequent association with dental (90%), central nervous system (33%) and ocular (35%) anomalies. The exact pathogenesis of this disorder remains unknown.Herein, we report a newborn girl with inflammatory vesiculobullous and warty skin lesions and a positive family history of IP, with blood leucocytosis (eosinophilia and also lymphocytosis), but no other extracutaneous findings.
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